Category: G40 - Epilepsy and recurrent seizures

 Chapter Notes

 G40

Epilepsy and recurrent seizures

the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled

conversion disorder with seizures (F44.5)

convulsions NOS (R56.9)

post traumatic seizures (R56.1)

seizure (convulsive) NOS (R56.9)

seizure of newborn (P90)

hippocampal sclerosis (G93.81)

mesial temporal sclerosis (G93.81)

temporal sclerosis (G93.81)

Todd's paralysis (G83.84)

 G40.0

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset

Benign childhood epilepsy with centrotemporal EEG spikes

Childhood epilepsy with occipital EEG paroxysms

adult onset localization-related epilepsy (G40.1-, G40.2-)

 G40.00

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset without intractability

 G40.001

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, with status epilepticus

 G40.009

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, without status epilepticus

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset NOS

 G40.01

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable

 G40.011

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, with status epilepticus

 G40.019

Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, without status epilepticus

 G40.1

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures

Attacks without alteration of consciousness

Epilepsia partialis continua [Kozhevnikof]

Simple partial seizures developing into secondarily generalized seizures

 G40.10

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures without intractability

 G40.101

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus

 G40.109

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures NOS

 G40.11

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable

 G40.111

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus

 G40.119

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus

 G40.2

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures

Attacks with alteration of consciousness, often with automatisms

Complex partial seizures developing into secondarily generalized seizures

 G40.20

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures without intractability

 G40.201

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus

 G40.209

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, without status epilepticus

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures NOS

 G40.21

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable

 G40.211

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, with status epilepticus

 G40.219

Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, without status epilepticus

 G40.3

Generalized idiopathic epilepsy and epileptic syndromes

Code also MERRF syndrome, if applicable (E88.42)

 G40.30

Generalized idiopathic epilepsy and epileptic syndromes, not intractable

Generalized idiopathic epilepsy and epileptic syndromes without intractability

 G40.301

Generalized idiopathic epilepsy and epileptic syndromes, not intractable, with status epilepticus

 G40.309

Generalized idiopathic epilepsy and epileptic syndromes, not intractable, without status epilepticus

Generalized idiopathic epilepsy and epileptic syndromes NOS

 G40.31

Generalized idiopathic epilepsy and epileptic syndromes, intractable

 G40.311

Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus

 G40.319

Generalized idiopathic epilepsy and epileptic syndromes, intractable, without status epilepticus

 G40.A

Absence epileptic syndrome

Childhood absence epilepsy [pyknolepsy]

Juvenile absence epilepsy

Absence epileptic syndrome, NOS

 G40.A0

Absence epileptic syndrome, not intractable

 G40.A01

Absence epileptic syndrome, not intractable, with status epilepticus

 G40.A09

Absence epileptic syndrome, not intractable, without status epilepticus

 G40.A1

Absence epileptic syndrome, intractable

 G40.A11

Absence epileptic syndrome, intractable, with status epilepticus

 G40.A19

Absence epileptic syndrome, intractable, without status epilepticus

 G40.B

Juvenile myoclonic epilepsy [impulsive petit mal]

 G40.B0

Juvenile myoclonic epilepsy, not intractable

 G40.B01

Juvenile myoclonic epilepsy, not intractable, with status epilepticus

 G40.B09

Juvenile myoclonic epilepsy, not intractable, without status epilepticus

 G40.B1

Juvenile myoclonic epilepsy, intractable

 G40.B11

Juvenile myoclonic epilepsy, intractable, with status epilepticus

 G40.B19

Juvenile myoclonic epilepsy, intractable, without status epilepticus

 G40.4

Other generalized epilepsy and epileptic syndromes

Epilepsy with grand mal seizures on awakening

Epilepsy with myoclonic absences

Epilepsy with myoclonic-astatic seizures

Grand mal seizure NOS

Nonspecific atonic epileptic seizures

Nonspecific clonic epileptic seizures

Nonspecific myoclonic epileptic seizures

Nonspecific tonic epileptic seizures

Nonspecific tonic-clonic epileptic seizures

Symptomatic early myoclonic encephalopathy

 G40.40

Other generalized epilepsy and epileptic syndromes, not intractable

Other generalized epilepsy and epileptic syndromes without intractability

Other generalized epilepsy and epileptic syndromes NOS

 G40.401

Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus

 G40.409

Other generalized epilepsy and epileptic syndromes, not intractable, without status epilepticus

 G40.41

Other generalized epilepsy and epileptic syndromes, intractable

 G40.411

Other generalized epilepsy and epileptic syndromes, intractable, with status epilepticus

 G40.419

Other generalized epilepsy and epileptic syndromes, intractable, without status epilepticus

 G40.42

Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

CDKL5

Use additional code, if known, to identify associated manifestations, such as:

cortical blindness (H47.61-)

global developmental delay (F88)

 G40.5

Epileptic seizures related to external causes

Epileptic seizures related to alcohol

Epileptic seizures related to drugs

Epileptic seizures related to hormonal changes

Epileptic seizures related to sleep deprivation

Epileptic seizures related to stress

Code also, if applicable, associated epilepsy and recurrent seizures (G40.-)

Use additional code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)

 G40.50

Epileptic seizures related to external causes, not intractable

 G40.501

Epileptic seizures related to external causes, not intractable, with status epilepticus

 G40.509

Epileptic seizures related to external causes, not intractable, without status epilepticus

Epileptic seizures related to external causes, NOS

 G40.8

Other epilepsy and recurrent seizures

Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized

Landau-Kleffner syndrome

 G40.80

Other epilepsy

 G40.801

Other epilepsy, not intractable, with status epilepticus

Other epilepsy without intractability with status epilepticus

 G40.802

Other epilepsy, not intractable, without status epilepticus

Other epilepsy NOS

Other epilepsy without intractability without status epilepticus

 G40.803

Other epilepsy, intractable, with status epilepticus

 G40.804

Other epilepsy, intractable, without status epilepticus

 G40.81

Lennox-Gastaut syndrome

 G40.811

Lennox-Gastaut syndrome, not intractable, with status epilepticus

 G40.812

Lennox-Gastaut syndrome, not intractable, without status epilepticus

 G40.813

Lennox-Gastaut syndrome, intractable, with status epilepticus

 G40.814

Lennox-Gastaut syndrome, intractable, without status epilepticus

 G40.82

Epileptic spasms

Infantile spasms

Salaam attacks

West's syndrome

 G40.821

Epileptic spasms, not intractable, with status epilepticus

 G40.822

Epileptic spasms, not intractable, without status epilepticus

 G40.823

Epileptic spasms, intractable, with status epilepticus

 G40.824

Epileptic spasms, intractable, without status epilepticus

 G40.83

Dravet syndrome

Polymorphic epilepsy in infancy (PMEI)

Severe myoclonic epilepsy in infancy (SMEI)

 G40.833

Dravet syndrome, intractable, with status epilepticus

 G40.834

Dravet syndrome, intractable, without status epilepticus

Dravet syndrome NOS

 G40.89

Other seizures

post traumatic seizures (R56.1)

recurrent seizures NOS (G40.909)

seizure NOS (R56.9)

 G40.9

Epilepsy, unspecified

 G40.90

Epilepsy, unspecified, not intractable

Epilepsy, unspecified, without intractability

 G40.901

Epilepsy, unspecified, not intractable, with status epilepticus

 G40.909

Epilepsy, unspecified, not intractable, without status epilepticus

Epilepsy NOS

Epileptic convulsions NOS

Epileptic fits NOS

Epileptic seizures NOS

Recurrent seizures NOS

Seizure disorder NOS

 G40.91

Epilepsy, unspecified, intractable

Intractable seizure disorder NOS

 G40.911

Epilepsy, unspecified, intractable, with status epilepticus

 G40.919

Epilepsy, unspecified, intractable, without status epilepticus