Category: D68 - Other coagulation defects

 Chapter Notes

 D68

Other coagulation defects

abnormal coagulation profile NOS (R79.1)

coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)

coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

 D68.0

Von Willebrand disease

capillary fragility (hereditary) (D69.8)

factor VIII deficiency NOS (D66)

factor VIII deficiency with functional defect (D66)

 D68.00

Von Willebrand disease, unspecified

 D68.01

Von Willebrand disease, type 1

Partial quantitative deficiency of von Willebrand factor

Type 1C von Willebrand disease

 D68.02

Von Willebrand disease, type 2

Qualitative defects of von Willebrand factor

 D68.020

Von Willebrand disease, type 2A

Qualitative defects of von Willebrand factor with decreased platelet adhesion and selective deficiency of high-molecular-weight multimers

 D68.021

Von Willebrand disease, type 2B

Qualitative defects of von Willebrand factor with high-molecular-weight von Willebrand factor loss

Qualitative defects of von Willebrand factor with hyper-adhesive forms

Qualitative defects of von Willebrand factor with increased affinity for platelet glycoprotein lb

 D68.022

Von Willebrand disease, type 2M

Qualitative defects of von Willebrand factor with defective platelet adhesion with a normal size distribution of von Willebrand factor multimers

 D68.023

Von Willebrand disease, type 2N

Qualitative defects of von Willebrand factor with defective von Willebrand factor to factor VIII binding

Qualitative defects of von Willebrand factor with markedly decreased affinity for factor VIII

 D68.029

Von Willebrand disease, type 2, unspecified

Qualitative defect in von Willebrand factor function, with no further subtyping

 D68.03

Von Willebrand disease, type 3

(Near) complete absence of von Willebrand factor

Total quantitative deficiency of von Willebrand factor

 D68.04

Acquired von Willebrand disease

Acquired von Willebrand syndrome

 D68.09

Other von Willebrand disease

Platelet-type von Willebrand disease

Pseudo-von Willebrand disease

Code also, if applicable, qualitative platelet defects (D69.1)

 D68.1

Hereditary factor XI deficiency

Hemophilia C

Plasma thromboplastin antecedent [PTA] deficiency

Rosenthal's disease

 D68.2

Hereditary deficiency of other clotting factors

AC globulin deficiency

Congenital afibrinogenemia

Deficiency of factor I [fibrinogen]

Deficiency of factor II [prothrombin]

Deficiency of factor V [labile]

Deficiency of factor VII [stable]

Deficiency of factor X [Stuart-Prower]

Deficiency of factor XII [Hageman]

Deficiency of factor XIII [fibrin stabilizing]

Dysfibrinogenemia (congenital)

Hypoproconvertinemia

Owren's disease

Proaccelerin deficiency

 D68.3

Hemorrhagic disorder due to circulating anticoagulants

 D68.31

Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors

 D68.311

Acquired hemophilia

Autoimmune hemophilia

Autoimmune inhibitors to clotting factors

Secondary hemophilia

 D68.312

Antiphospholipid antibody with hemorrhagic disorder

Lupus anticoagulant (LAC) with hemorrhagic disorder

Systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder

antiphospholipid antibody, finding without diagnosis (R76.0)

antiphospholipid antibody syndrome (D68.61)

antiphospholipid antibody with hypercoagulable state (D68.61)

lupus anticoagulant (LAC) finding without diagnosis (R76.0)

lupus anticoagulant (LAC) with hypercoagulable state (D68.62)

systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)

systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.62)

 D68.318

Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors

Antithromboplastinemia

Antithromboplastinogenemia

Hemorrhagic disorder due to intrinsic increase in antithrombin

Hemorrhagic disorder due to intrinsic increase in anti-VIIIa

Hemorrhagic disorder due to intrinsic increase in anti-IXa

Hemorrhagic disorder due to intrinsic increase in anti-XIa

 D68.32

Hemorrhagic disorder due to extrinsic circulating anticoagulants

Drug-induced hemorrhagic disorder

Hemorrhagic disorder due to increase in anti-IIa

Hemorrhagic disorder due to increase in anti-Xa

Hyperheparinemia

Use additional code for adverse effect, if applicable, to identify drug (T45.515, T45.525)

 D68.4

Acquired coagulation factor deficiency

Deficiency of coagulation factor due to liver disease

Deficiency of coagulation factor due to vitamin K deficiency

vitamin K deficiency of newborn (P53)

 D68.5

Primary thrombophilia

Primary hypercoagulable states

antiphospholipid syndrome (D68.61)

lupus anticoagulant (D68.62)

secondary activated protein C resistance (D68.69)

secondary antiphospholipid antibody syndrome (D68.69)

secondary lupus anticoagulant with hypercoagulable state (D68.69)

secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)

systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)

systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)

thrombotic thrombocytopenic purpura (M31.19)

 D68.51

Activated protein C resistance

Factor V Leiden mutation

 D68.52

Prothrombin gene mutation

 D68.59

Other primary thrombophilia

Antithrombin III deficiency

Hypercoagulable state NOS

Primary hypercoagulable state NEC

Primary thrombophilia NEC

Protein C deficiency

Protein S deficiency

Thrombophilia NOS

 D68.6

Other thrombophilia

Other hypercoagulable states

diffuse or disseminated intravascular coagulation [DIC] (D65)

heparin induced thrombocytopenia (HIT) (D75.82-)

hyperhomocysteinemia (E72.11)

 D68.61

Antiphospholipid syndrome

Anticardiolipin syndrome

Antiphospholipid antibody syndrome

anti-phospholipid antibody, finding without diagnosis (R76.0)

anti-phospholipid antibody with hemorrhagic disorder (D68.312)

lupus anticoagulant syndrome (D68.62)

 D68.62

Lupus anticoagulant syndrome

Lupus anticoagulant

Presence of systemic lupus erythematosus [SLE] inhibitor

anticardiolipin syndrome (D68.61)

antiphospholipid syndrome (D68.61)

lupus anticoagulant (LAC) finding without diagnosis (R76.0)

lupus anticoagulant (LAC) with hemorrhagic disorder (D68.312)

 D68.69

Other thrombophilia

Hypercoagulable states NEC

Secondary hypercoagulable state NOS

 D68.8

Other specified coagulation defects

hemorrhagic disease of newborn (P53)

 D68.9

Coagulation defect, unspecified