Category: D56 - Thalassemia

 Chapter Notes

 D56

Thalassemia

sickle-cell thalassemia (D57.4-)

 D56.0

Alpha thalassemia

Alpha thalassemia major

Hemoglobin H Constant Spring

Hemoglobin H disease

Hydrops fetalis due to alpha thalassemia

Severe alpha thalassemia

Triple gene defect alpha thalassemia

Use additional code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)

alpha thalassemia trait or minor (D56.3)

asymptomatic alpha thalassemia (D56.3)

hydrops fetalis due to isoimmunization (P56.0)

hydrops fetalis not due to immune hemolysis (P83.2)

 D56.1

Beta thalassemia

Beta thalassemia major

Cooley's anemia

Homozygous beta thalassemia

Severe beta thalassemia

Thalassemia intermedia

Thalassemia major

beta thalassemia minor (D56.3)

beta thalassemia trait (D56.3)

delta-beta thalassemia (D56.2)

hemoglobin E-beta thalassemia (D56.5)

sickle-cell beta thalassemia (D57.4-)

 D56.2

Delta-beta thalassemia

Homozygous delta-beta thalassemia

delta-beta thalassemia minor (D56.3)

delta-beta thalassemia trait (D56.3)

 D56.3

Thalassemia minor

Alpha thalassemia minor

Alpha thalassemia silent carrier

Alpha thalassemia trait

Beta thalassemia minor

Beta thalassemia trait

Delta-beta thalassemia minor

Delta-beta thalassemia trait

Thalassemia trait NOS

alpha thalassemia (D56.0)

beta thalassemia (D56.1)

delta-beta thalassemia (D56.2)

hemoglobin E-beta thalassemia (D56.5)

sickle-cell trait (D57.3)

 D56.4

Hereditary persistence of fetal hemoglobin [HPFH]

 D56.5

Hemoglobin E-beta thalassemia

beta thalassemia (D56.1)

beta thalassemia minor (D56.3)

beta thalassemia trait (D56.3)

delta-beta thalassemia (D56.2)

delta-beta thalassemia trait (D56.3)

hemoglobin E disease (D58.2)

other hemoglobinopathies (D58.2)

sickle-cell beta thalassemia (D57.4-)

 D56.8

Other thalassemias

Dominant thalassemia

Hemoglobin C thalassemia

Mixed thalassemia

Thalassemia with other hemoglobinopathy

hemoglobin C disease (D58.2)

hemoglobin E disease (D58.2)

other hemoglobinopathies (D58.2)

sickle-cell anemia (D57.-)

sickle-cell thalassemia (D57.4-)

 D56.9

Thalassemia, unspecified

Mediterranean anemia (with other hemoglobinopathy)