Category: Q56 - Indeterminate sex and pseudohermaphroditism

 Chapter Notes

 Section Notes

 Q56

Indeterminate sex and pseudohermaphroditism

46,XX true hermaphrodite (Q99.1)

androgen insensitivity syndrome (E34.5-)

chimera 46,XX/46,XY true hermaphrodite (Q99.0)

female pseudohermaphroditism with adrenocortical disorder (E25.-)

pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)

pure gonadal dysgenesis (Q99.1)

 Q56.0

Hermaphroditism, not elsewhere classified

Ovotestis

 Q56.1

Male pseudohermaphroditism, not elsewhere classified

46, XY with streak gonads

Male pseudohermaphroditism NOS

 Q56.2

Female pseudohermaphroditism, not elsewhere classified

Female pseudohermaphroditism NOS

 Q56.3

Pseudohermaphroditism, unspecified

 Q56.4

Indeterminate sex, unspecified

Ambiguous genitalia