Category: M35 - Other systemic involvement of connective tissue

 Chapter Notes

 Section Notes

 M35

Other systemic involvement of connective tissue

reactive perforating collagenosis (L87.1)

 M35.0

Sjögren syndrome

Sicca syndrome

Use additional code to identify associated manifestations

dry mouth, unspecified (R68.2)

 M35.00

Sjögren syndrome, unspecified

 M35.01

Sjögren syndrome with keratoconjunctivitis

 M35.02

Sjögren syndrome with lung involvement

 M35.03

Sjögren syndrome with myopathy

 M35.04

Sjögren syndrome with tubulo-interstitial nephropathy

Renal tubular acidosis in sicca syndrome

 M35.05

Sjögren syndrome with inflammatory arthritis

 M35.06

Sjögren syndrome with peripheral nervous system involvement

 M35.07

Sjögren syndrome with central nervous system involvement

 M35.08

Sjögren syndrome with gastrointestinal involvement

 M35.0A

Sjögren syndrome with glomerular disease

 M35.0B

Sjögren syndrome with vasculitis

 M35.0C

Sjögren syndrome with dental involvement

 M35.09

Sjögren syndrome with other organ involvement

 M35.1

Other overlap syndromes

Mixed connective tissue disease

polyangiitis overlap syndrome (M30.8)

 M35.2

Behçet's disease

 M35.3

Polymyalgia rheumatica

polymyalgia rheumatica with giant cell arteritis (M31.5)

 M35.4

Diffuse (eosinophilic) fasciitis

 M35.5

Multifocal fibrosclerosis

 M35.6

Relapsing panniculitis [Weber-Christian]

lupus panniculitis (L93.2)

panniculitis NOS (M79.3-)

 M35.7

Hypermobility syndrome

Familial ligamentous laxity

ligamentous laxity, NOS (M24.2-)

Ehlers-Danlos syndromes (Q79.6-)

 M35.8

Other specified systemic involvement of connective tissue

 M35.81

Multisystem inflammatory syndrome

MIS-A

MIS-C

Multisystem inflammatory syndrome in adults

Multisystem inflammatory syndrome in children

Pediatric inflammatory multisystem syndrome

PIMS

Code first, if applicable, COVID-19 (U07.1)

Code also any associated complications such as:

acute hepatic failure (K72.0-)

acute kidney failure (N17.-)

acute myocarditis (I40.-)

acute respiratory distress syndrome (J80)

cardiac arrhythmia (I47-I49.-)

pneumonia due to COVID-19 (J12.82)

severe sepsis (R65.2-)

viral cardiomyopathy (B33.24)

viral pericarditis (B33.23)

Use additional code, if applicable, for:

exposure to COVID-19 or SARS-CoV-2 infection (Z20.822)

personal history of COVID-19 (Z86.16)

post COVID-19 condition (U09.9)

 M35.89

Other specified systemic involvement of connective tissue

 M35.9

Systemic involvement of connective tissue, unspecified

Autoimmune disease (systemic) NOS

Collagen (vascular) disease NOS