Category: J84 - Other interstitial pulmonary diseases
Chapter Notes
Other interstitial pulmonary diseases
drug-induced interstitial lung disorders (J70.2-J70.4)
interstitial emphysema (J98.2)
lung diseases due to external agents (J60-J70)
Alveolar and parieto-alveolar conditions
Alveolar proteinosis
Pulmonary alveolar microlithiasis
Idiopathic pulmonary hemosiderosis
Essential brown induration of lung
Code first underlying disease, such as:
disorders of iron metabolism (E83.1-)
acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81)
Other alveolar and parieto-alveolar conditions
Other interstitial pulmonary diseases with fibrosis
pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
pulmonary fibrosis (chronic) following radiation (J70.1)
Pulmonary fibrosis, unspecified
Capillary fibrosis of lung
Cirrhosis of lung (chronic) NOS
Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
Induration of lung (chronic) NOS
Postinflammatory pulmonary fibrosis
Idiopathic interstitial pneumonia
lymphoid interstitial pneumonia (J84.2)
pneumocystis pneumonia (B59)
Idiopathic interstitial pneumonia, not otherwise specified
Idiopathic pulmonary fibrosis
Cryptogenic fibrosing alveolitis
Idiopathic fibrosing alveolitis
Idiopathic non-specific interstitial pneumonitis
non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89)
Acute interstitial pneumonitis
Hamman-Rich syndrome
Respiratory bronchiolitis interstitial lung disease
Cryptogenic organizing pneumonia
organizing pneumonia NOS, or due to known underlying cause (J84.89)
Desquamative interstitial pneumonia
Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
Progressive fibrotic interstitial lung disease
rheumatoid arthritis (M05.00-M06.9)
sarcoidosis (D86.-)
systemic connective tissue disorders (M30-M36)
Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
Organizing pneumonia due to collagen vascular disease
Organizing pneumonia in diseases classified elsewhere
progressive systemic sclerosis (M34.0)
systemic lupus erythematosis (M32.0-M32.9)
Lymphoid interstitial pneumonia
Lymphoid interstitial pneumonitis
Other specified interstitial pulmonary diseases
exogenous lipoid pneumonia (J69.1)
unspecified lipoid pneumonia (J69.1)
Lymphangioleiomyomatosis
Lymphangiomyomatosis
Adult pulmonary Langerhans cell histiocytosis
Adult PLCH
Surfactant mutations of the lung
Other interstitial lung diseases of childhood
Neuroendocrine cell hyperplasia of infancy
Pulmonary interstitial glycogenosis
Alveolar capillary dysplasia with vein misalignment
Endogenous lipoid pneumonia
Interstitial pneumonitis
Non-specific interstitial pneumonitis NOS
Organizing pneumonia NOS
Code first, if applicable:
poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
underlying cause of pneumonopathy, if known
Use additional code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced
cryptogenic organizing pneumonia (J84.116)
idiopathic non-specific interstitial pneumonitis (J84.113)
lipoid pneumonia, exogenous or unspecified (J69.1)
Interstitial pulmonary disease, unspecified
Interstitial pneumonia NOS
