Category: I27 - Other pulmonary heart diseases

 Chapter Notes

 I27

Other pulmonary heart diseases

 I27.0

Primary pulmonary hypertension

Heritable pulmonary arterial hypertension

Idiopathic pulmonary arterial hypertension

Primary group 1 pulmonary hypertension

Primary pulmonary arterial hypertension

persistent pulmonary hypertension of newborn (P29.30)

pulmonary hypertension NOS (I27.20)

secondary pulmonary arterial hypertension (I27.21)

secondary pulmonary hypertension (I27.29)

 I27.1

Kyphoscoliotic heart disease

 I27.2

Other secondary pulmonary hypertension

Code also associated underlying condition

Eisenmenger's syndrome (I27.83)

 I27.20

Pulmonary hypertension, unspecified

Pulmonary hypertension NOS

 I27.21

Secondary pulmonary arterial hypertension

(Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS

(Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension

Code also associated conditions if applicable, or adverse effects of drugs or toxins, such as:

adverse effect of appetite depressants (T50.5X5)

congenital heart disease (Q20-Q28)

human immunodeficiency virus [HIV] disease (B20)

polymyositis (M33.2-)

portal hypertension (K76.6)

rheumatoid arthritis (M05.-)

schistosomiasis (B65.-)

Sjögren syndrome (M35.0-)

systemic sclerosis (M34.-)

 I27.22

Pulmonary hypertension due to left heart disease

Group 2 pulmonary hypertension

Code also associated left heart disease, if known, such as:

multiple valve disease (I08.-)

rheumatic mitral valve diseases (I05.-)

rheumatic aortic valve diseases (I06.-)

 I27.23

Pulmonary hypertension due to lung diseases and hypoxia

Group 3 pulmonary hypertension

Code also associated lung disease, if known, such as:

bronchiectasis (J47.-)

cystic fibrosis with pulmonary manifestations (E84.0)

interstitial lung disease (J84.-)

pleural effusion (J90)

sleep apnea (G47.3-)

 I27.24

Chronic thromboembolic pulmonary hypertension

Group 4 pulmonary hypertension

Code also associated pulmonary embolism, if applicable (I26.-, I27.82)

 I27.29

Other secondary pulmonary hypertension

Group 5 pulmonary hypertension

Pulmonary hypertension with unclear multifactorial mechanisms

Pulmonary hypertension due to hematologic disorders

Pulmonary hypertension due to metabolic disorders

Pulmonary hypertension due to other systemic disorders

Code also other associated disorders, if known, such as:

chronic myeloid leukemia (C92.10-C92.22)

essential thrombocythemia (D47.3)

Gaucher disease (E75.22)

hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)

hyperthyroidism (E05.-)

hypothyroidism (E00-E03)

polycythemia vera (D45)

sarcoidosis (D86.-)

 I27.8

Other specified pulmonary heart diseases

 I27.81

Cor pulmonale (chronic)

Cor pulmonale NOS

Code also, if applicable, right heart failure (I50.81-)

acute cor pulmonale (I26.0-)

 I27.82

Chronic pulmonary embolism

Use additional code, if applicable, for associated long-term (current) use of anticoagulants (Z79.01)

personal history of pulmonary embolism (Z86.711)

 I27.83

Eisenmenger's syndrome

Eisenmenger's complex

(Irreversible) Eisenmenger's disease

Pulmonary hypertension with right to left shunt related to congenital heart disease

Code also underlying heart defect, if known, such as:

atrial septal defect (Q21.1-)

Eisenmenger's defect (Q21.8)

patent ductus arteriosus (Q25.0)

ventricular septal defect (Q21.0)

 I27.89

Other specified pulmonary heart diseases

 I27.9

Pulmonary heart disease, unspecified

Chronic cardiopulmonary disease