Category: D89 - Other disorders involving the immune mechanism, not elsewhere classified

 Chapter Notes

 Section Notes

 D89

Other disorders involving the immune mechanism, not elsewhere classified

hyperglobulinemia NOS (R77.1)

monoclonal gammopathy (of undetermined significance) (D47.2)

transplant failure and rejection (T86.-)

 D89.0

Polyclonal hypergammaglobulinemia

Benign hypergammaglobulinemic purpura

Polyclonal gammopathy NOS

 D89.1

Cryoglobulinemia

Cryoglobulinemic purpura

Cryoglobulinemic vasculitis

Essential cryoglobulinemia

Idiopathic cryoglobulinemia

Mixed cryoglobulinemia

Primary cryoglobulinemia

Secondary cryoglobulinemia

 D89.2

Hypergammaglobulinemia, unspecified

 D89.3

Immune reconstitution syndrome

Immune reconstitution inflammatory syndrome [IRIS]

Use additional code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)

 D89.4

Mast cell activation syndrome and related disorders

aggressive systemic mastocytosis (C96.21)

congenital cutaneous mastocytosis (Q82.2)

(non-congenital) cutaneous mastocytosis (D47.01)

(indolent) systemic mastocytosis (D47.02)

malignant mast cell neoplasm (C96.2-)

malignant mastocytoma (C96.29)

mast cell leukemia (C94.3-)

mast cell sarcoma (C96.22)

mastocytoma NOS (D47.09)

other mast cell neoplasms of uncertain behavior (D47.09)

systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)

 D89.40

Mast cell activation, unspecified

Mast cell activation disorder, unspecified

Mast cell activation syndrome, NOS

 D89.41

Monoclonal mast cell activation syndrome

 D89.42

Idiopathic mast cell activation syndrome

 D89.43

Secondary mast cell activation

Secondary mast cell activation syndrome

Code also underlying etiology, if known

 D89.44

Hereditary alpha tryptasemia

Use additional code, if applicable, for:

allergy status, other than to drugs and biological substances (Z91.0-)

personal history of anaphylaxis (Z87.892)

 D89.49

Other mast cell activation disorder

Other mast cell activation syndrome

 D89.8

Other specified disorders involving the immune mechanism, not elsewhere classified

 D89.81

Graft-versus-host disease

Code first underlying cause, such as:

complications of transplanted organs and tissue (T86.-)

complications of blood transfusion (T80.89)

Use additional code to identify associated manifestations, such as:

desquamative dermatitis (L30.8)

diarrhea (R19.7)

elevated bilirubin (R17)

hair loss (L65.9)

 D89.810

Acute graft-versus-host disease

 D89.811

Chronic graft-versus-host disease

 D89.812

Acute on chronic graft-versus-host disease

 D89.813

Graft-versus-host disease, unspecified

 D89.82

Autoimmune lymphoproliferative syndrome [ALPS]

 D89.83

Cytokine release syndrome

Code first underlying cause, such as:

complications following infusion, transfusion and therapeutic injection (T80.89-)

complications of transplanted organs and tissue (T86.-)

Use additional code to identify associated manifestations

 D89.831

Cytokine release syndrome, grade 1

 D89.832

Cytokine release syndrome, grade 2

 D89.833

Cytokine release syndrome, grade 3

 D89.834

Cytokine release syndrome, grade 4

 D89.835

Cytokine release syndrome, grade 5

 D89.839

Cytokine release syndrome, grade unspecified

 D89.84

IgG4-related disease

Immunoglobulin G4-related disease

 D89.89

Other specified disorders involving the immune mechanism, not elsewhere classified

human immunodeficiency virus disease (B20)

 D89.9

Disorder involving the immune mechanism, unspecified

Immune disease NOS