Category: D57 - Sickle-cell disorders

 Chapter Notes

 D57

Sickle-cell disorders

Use additional code for any associated fever (R50.81)

other hemoglobinopathies (D58.-)

 D57.0

Hb-SS disease with crisis

Sickle-cell disease with crisis

Hb-SS disease with (vaso-occlusive) pain

 D57.00

Hb-SS disease with crisis, unspecified

Hb-SS disease with (painful) crisis NOS

Hb-SS disease with (vaso-occlusive) pain NOS

 D57.01

Hb-SS disease with acute chest syndrome

 D57.02

Hb-SS disease with splenic sequestration

 D57.03

Hb-SS disease with cerebral vascular involvement

Code also, if applicable, cerebral infarction (I63.-)

 D57.04

Hb-SS disease with dactylitis

 D57.09

Hb-SS disease with crisis with other specified complication

Use additional code to identify complications, such as:

cholelithiasis (K80.-)

priapism (N48.32)

 D57.1

Sickle-cell disease without crisis

Hb-SS disease without crisis

Sickle-cell anemia NOS

Sickle-cell disease NOS

Sickle-cell disorder NOS

 D57.2

Sickle-cell/Hb-C disease

Hb-SC disease

Hb-S/Hb-C disease

 D57.20

Sickle-cell/Hb-C disease without crisis

 D57.21

Sickle-cell/Hb-C disease with crisis

 D57.211

Sickle-cell/Hb-C disease with acute chest syndrome

 D57.212

Sickle-cell/Hb-C disease with splenic sequestration

 D57.213

Sickle-cell/Hb-C disease with cerebral vascular involvement

Code also, if applicable, cerebral infarction (I63.-)

 D57.214

Sickle-cell/Hb-C disease with dactylitis

 D57.218

Sickle-cell/Hb-C disease with crisis with other specified complication

Use additional code to identify complications, such as:

cholelithiasis (K80.-)

priapism (N48.32)

 D57.219

Sickle-cell/Hb-C disease with crisis, unspecified

Sickle-cell/Hb-C disease with crisis NOS

Sickle-cell/Hb-C disease with (vaso-occlusive) pain NOS

 D57.3

Sickle-cell trait

Hb-S trait

Heterozygous hemoglobin S

 D57.4

Sickle-cell thalassemia

Sickle-cell beta thalassemia

Thalassemia Hb-S disease

 D57.40

Sickle-cell thalassemia without crisis

Microdrepanocytosis

Sickle-cell thalassemia NOS

 D57.41

Sickle-cell thalassemia, unspecified, with crisis

Sickle-cell thalassemia with (painful) crisis NOS

Sickle-cell thalassemia with (vaso-occlusive) pain NOS

 D57.411

Sickle-cell thalassemia, unspecified, with acute chest syndrome

 D57.412

Sickle-cell thalassemia, unspecified, with splenic sequestration

 D57.413

Sickle-cell thalassemia, unspecified, with cerebral vascular involvement

Code also, if applicable cerebral infarction (I63.-)

 D57.414

Sickle-cell thalassemia, unspecified, with dactylitis

 D57.418

Sickle-cell thalassemia, unspecified, with crisis with other specified complication

Use additional code to identify complications, such as:

cholelithiasis (K80.-)

priapism (N48.32)

 D57.419

Sickle-cell thalassemia, unspecified, with crisis

Sickle-cell thalassemia with (painful) crisis NOS

Sickle-cell thalassemia with (vaso-occlusive) pain NOS

 D57.42

Sickle-cell thalassemia beta zero without crisis

HbS-beta zero without crisis

Sickle-cell beta zero without crisis

 D57.43

Sickle-cell thalassemia beta zero with crisis

HbS-beta zero with crisis

Sickle-cell beta zero with crisis

 D57.431

Sickle-cell thalassemia beta zero with acute chest syndrome

HbS-beta zero with acute chest syndrome

Sickle-cell beta zero with acute chest syndrome

 D57.432

Sickle-cell thalassemia beta zero with splenic sequestration

HbS-beta zero with splenic sequestration

Sickle-cell beta zero with splenic sequestration

 D57.433

Sickle-cell thalassemia beta zero with cerebral vascular involvement

HbS-beta zero with cerebral vascular involvement

Sickle-cell beta zero with cerebral vascular involvement

Code also, if applicable cerebral infarction (I63.-)

 D57.434

Sickle-cell thalassemia beta zero with dactylitis

 D57.438

Sickle-cell thalassemia beta zero with crisis with other specified complication

HbS-beta zero with other specified complication

Sickle-cell beta zero with other specified complication

Use additional code to identify complications, such as:

cholelithiasis (K80.-)

priapism (N48.32)

 D57.439

Sickle-cell thalassemia beta zero with crisis, unspecified

HbS-beta zero with other specified complication

Sickle-cell beta zero with crisis unspecified

Sickle-cell thalassemia beta zero with (painful) crisis NOS

Sickle-cell thalassemia beta zero with (vaso-occlusive) pain NOS

 D57.44

Sickle-cell thalassemia beta plus without crisis

HbS-beta plus without crisis

Sickle-cell beta plus without crisis

 D57.45

Sickle-cell thalassemia beta plus with crisis

HbS-beta plus with crisis

Sickle-cell beta plus with crisis

 D57.451

Sickle-cell thalassemia beta plus with acute chest syndrome

HbS-beta plus with acute chest syndrome

Sickle-cell beta plus with acute chest syndrome

 D57.452

Sickle-cell thalassemia beta plus with splenic sequestration

HbS-beta plus with splenic sequestration

Sickle-cell beta plus with splenic sequestration

 D57.453

Sickle-cell thalassemia beta plus with cerebral vascular involvement

HbS-beta plus with cerebral vascular involvement

Sickle-cell beta plus with cerebral vascular involvement

Code also, if applicable cerebral infarction (I63.-)

 D57.454

Sickle-cell thalassemia beta plus with dactylitis

 D57.458

Sickle-cell thalassemia beta plus with crisis with other specified complication

HbS-beta plus with crisis with other specified complication

Sickle-cell beta plus with crisis with other specified complication

Use additional code to identify complications, such as:

cholelithiasis (K80.-)

priapism (N48.32)

 D57.459

Sickle-cell thalassemia beta plus with crisis, unspecified

HbS-beta plus with crisis with unspecified complication

Sickle-cell beta plus with crisis with unspecified complication

Sickle-cell thalassemia beta plus with (painful) crisis NOS

Sickle-cell thalassemia beta plus with (vaso-occlusive) pain NOS

 D57.8

Other sickle-cell disorders

Hb-SD disease

Hb-SE disease

 D57.80

Other sickle-cell disorders without crisis

 D57.81

Other sickle-cell disorders with crisis

 D57.811

Other sickle-cell disorders with acute chest syndrome

 D57.812

Other sickle-cell disorders with splenic sequestration

 D57.813

Other sickle-cell disorders with cerebral vascular involvement

Code also, if applicable: cerebral infarction (I63.-)

 D57.814

Other sickle-cell disorders with dactylitis

 D57.818

Other sickle-cell disorders with crisis with other specified complication

Use additional code to identify complications, such as:

cholelithiasis (K80.-)

priapism (N48.32)

 D57.819

Other sickle-cell disorders with crisis, unspecified

Other sickle-cell disorders with crisis NOS

Other sickle-cell disorders with (vaso-occlusive) pain NOS