Category: D47 - Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
Chapter Notes
Section Notes
Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
Mast cell neoplasms of uncertain behavior
congenital cutaneous mastocytosis (Q82.2)
histiocytic neoplasms of uncertain behavior (D47.Z9)
malignant mast cell neoplasm (C96.2-)
Cutaneous mastocytosis
Diffuse cutaneous mastocytosis
Maculopapular cutaneous mastocytosis
Solitary mastocytoma
Telangiectasia macularis eruptiva perstans
Urticaria pigmentosa
congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
congenital urticaria pigmentosa (Q82.2)
extracutaneous mastocytoma (D47.09)
Systemic mastocytosis
Indolent systemic mastocytosis
Isolated bone marrow mastocytosis
Smoldering systemic mastocytosis
Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code also, if applicable, any associated hematological non-mast cell lineage disease, such as:
acute myeloid leukemia (C92.6-, C92.A-)
chronic myelomonocytic leukemia (C93.1-)
essential thrombocytosis (D47.3)
hypereosinophilic syndrome (D72.1)
myelodysplastic syndrome (D46.9)
myeloproliferative syndrome (D47.1)
non-Hodgkin lymphoma (C82-C85)
plasma cell myeloma (C90.0-)
polycythemia vera (D45)
aggressive systemic mastocytosis (C96.21)
mast cell leukemia (C94.3-)
Other mast cell neoplasms of uncertain behavior
Extracutaneous mastocytoma
Mast cell tumor NOS
Mastocytoma NOS
Mastocytosis NOS
Chronic myeloproliferative disease
Chronic neutrophilic leukemia
Myeloproliferative disease, unspecified
atypical chronic myeloid leukemia BCR/ABL-negative (C92.2-)
chronic myeloid leukemia BCR/ABL-positive (C92.1-)
myelofibrosis NOS (D75.81)
myelophthisic anemia (D61.82)
myelophthisis (D61.82)
secondary myelofibrosis NOS (D75.81)
Monoclonal gammopathy
Monoclonal gammopathy of undetermined significance [MGUS]
Essential (hemorrhagic) thrombocythemia
Essential thrombocytosis
Idiopathic hemorrhagic thrombocythemia
Primary thrombocytosis
reactive thrombocytosis (D75.838)
secondary thrombocytosis (D75.838)
thrombocythemia NOS (D75.839)
thrombocytosis NOS (D75.839)
Osteomyelofibrosis
Chronic idiopathic myelofibrosis
Myelofibrosis (idiopathic) (with myeloid metaplasia)
Myelosclerosis (megakaryocytic) with myeloid metaplasia
Secondary myelofibrosis in myeloproliferative disease
acute myelofibrosis (C94.4-)
Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
Post-transplant lymphoproliferative disorder (PTLD)
Code first complications of transplanted organs and tissue (T86.-)
Castleman disease
Code also, if applicable, human herpesvirus 8 infection (B10.89)
Kaposi's sarcoma (C46.-)
Histiocytic tumors of uncertain behavior
Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified
Lymphoproliferative disease NOS
